Congenital absence of the portal vein with splenomegaly in a young woman (Case Report)
Abstract: Congenital Absence
of the Portal Vein (CAPV) is a rare anomaly in which the intestinal and splenic
venous drainage bypasses the liver and drains into the systemic veins through
various venous shunts. We present a case of a 32-year-old woman with this
malformation, the patient experienced hematemesis and melena repetitively and
had splenomegaly and hypersplenism. The angiography demonstrated absence of
portal vein. Splenectomy was performed to reduce the pressure of the veins
around stomach and to correct the hypersplenism. In endoscopy examination six
months after surgery, the esophageal varices had disappear and the size of
gastric varices had decrease.
Author: Murnizal Dahlan, Indah
Situmorang
Journal Code: jpkedokterangg050117
